Introduction:

Hirschsprung’s disease could involve a complex diagnosis and treatment. It requires long-term multidisciplinary management practices and vast experience in order to minimize acute morbidity.

Goals:

Study the epidemiology of patients with Hirschsprung’s disease at the Pereira Rossell Pediatric Hospital during 10 years (2006-2016) and identify their complications and long-term outcomes.

Materials and methods:

we reviewed the medical records between January 2006 and July 2016. We studied different variables and compared the evolution after performing the different surgical techniques. We used Fisher’s exact test and Chi square test as statistical methods.

Results:

we analyzed 30 medical records in this period, 22 males and 8 females. 16 patients had been diagnosed through aspiration biopsy, 11 through surgical biopsy and in one case the diagnosis was reached through anorectal manometry. 24 patients were diagnosed before the first year of life, and 19 received surgery before the first year of life. In the case of 23 patients, the disease involved rectosigmoid extension. The La Torre Mondragón technique was performed in 14 cases and the Soave technique or its Soave/Boley variant was performed in 9 cases.

Conclusion:

endoanal is the most used technique for the rectosigmoid extension pathology and it seems to be the technique of choice in the last years. Although we have not been able to fully assess patients operated using the De La Torre technique, we believe that it has many advantages in avoiding the abdominal approach. We have identified clear areas for improvement, such as the importance of diagnosis and early treatment, the need for well-established networks and long-term control for this type of pathology. We value the surgical team’s versatility when using different techniques customized to the patients’ needs.

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