Resumo

VENTURA, Verónica et al. Brugada Syndrome: report of two cases. Arch. Med Int [online]. 2015, vol.37, n. 3, pp.131-134. ISSN 0250-3816.

Abstract   Since its introduction as a clinical entity by the Brugada brothers in the 90s, the Brugada syndrome has generated great interest due to their association with an increased risk of ventricular arrhythmias and sudden death in young patients with structurally normal heart. This is a dominant genetic disease, autosomal that determines abnormalities in ion channels in myocardial tissue. ECG has a characteristic presentation, its main clinical manifestations syncope and sudden cardiac death. The presence of electrocardiographic pattern only in clinical manifestations absence should not be considered as a Brugada syndrome but as a Brugada pattern. The only available and effective treatment is the implantation of a permanent cardioverter defibrillator. Our interest is an upgrade of the issue based on two clinical cases that we attended.

Palavras-chave : Brugada syndrome; Syncope; Sudden cardiac death.